Pulmonary Hypertension: Treatments

How is pulmonary hypertension treated?

The Pulmonary Hypertension Program at Children's Hospital's Colorado has been treating children with the condition for more than 25 years. There are many treatment options for kids and young adults with pulmonary hypertension (sometimes called "PH" for short).

If the hypertension is secondary (meaning it is the result of another condition), the best treatment plan is exploration and treatment of contributing conditions. This may include repair of the underlying congenital heart defects, treatment of lung disease, as well as addressing less common secondary causes.

Symptoms and severity of the disease vary among all children with pulmonary hypertension. PH is a disease that can progress over time, especially if not properly diagnosed, monitored, or treated.

Although there is no cure for many types of pulmonary hypertension, treatments are available that can help lessen symptoms and improve your child's everyday life. Treatment options include:

  • Inhaled nitric oxide
  • Calcium channel blockers
  • Intravenous or inhaled epoprostenol (Flolan)
  • Intravenous and subcutaneous treprostinil (Remodulin)
  • Bosentan (Tracleer)
  • Ambrisentan (Letairis)
  • Sildenafil (Revatio)
  • Tadalafil (Adcirca)
  • Participation in clinical trial studies

Living with pulmonary hypertension

There is currently no cure for many forms of pulmonary hypertension, although close follow-up by a specialist with experience in treating PH can help your child live as normal a life as possible by monitoring your child's pulmonary pressures and response to medications.

Learn more about our Pulmonary Hypertension Program.